Ectopic Meningioma
Synonyms: Ectopic meningioma and meningothelial hamartoma
Extracranial meningioma - rare
Quick Facts
Behaviour
Benign
Category
Soft tissue
Synonyms
Ectopic meningioma and meningothelial hamartoma
Category
Soft tissue
Behaviour
Benign
Gender
Female
Tissue of Origin
Neural
Epidemiology
- Rare extracranial meningioma
- Soft tissue, skin, or bone outside CNS
- Female predominance
- All ages
Clinical Features
- Soft tissue mass at extracranial location
- Often scalp, orbit, or paraspinal
- Usually slow growing
Location
- Scalp
- Orbit
- Paraspinal region
- Sinonasal tract
Imaging
MRI: enhancing soft tissue mass with meningothelial features
Pathology
- Meningothelial whorls and psammoma bodies
- EMA positive
- SSTR2A positive
Genetics
NF2 mutations in some cases
Treatment
Surgical excision
Prognosis
- Excellent for benign lesions
- Rare malignant transformation
Key Points
- Extracranial meningioma - rare
- Scalp and orbit most common sites
- Histologically identical to intracranial meningioma
Workup - Blood Tests
None specific
Workup - Local Imaging
MRI with contrast
Workup - Biopsy
Excisional biopsy
Workup - Staging
MRI brain to exclude primary intracranial origin
Medical disclaimer
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