Desmoplastic Fibroblastoma
Synonyms: Collagenous fibroma
Benign collagenous tumour
Quick Facts
Behaviour
Benign
Category
Soft tissue
Synonyms
Collagenous fibroma
Category
Soft tissue
Behaviour
Benign
Gender
Male
Tissue of Origin
Fibrous
Epidemiology
- Rare benign fibroblastic tumour
- Middle-aged to elderly adults (4th-7th decades)
Clinical Features
- Painless firm subcutaneous or deep soft tissue nodule
- Slowly growing
- Well-circumscribed
Location
- Shoulder girdle
- Upper and lower extremities
- Back
Imaging
MRI: Well-circumscribed, hypointense on all sequences due to dense collagen
Pathology
- Paucicellular fibrous tumour with abundant collagen
- Spindle fibroblasts in myxocollagenous stroma
Genetics
FOSL1 rearrangement (11q12)
Treatment
Simple excision curative
Prognosis
Excellent - benign with no recurrence
Key Points
- Benign collagenous tumour
- FOSL1 rearrangement is defining
- Simple excision curative - no recurrence
Workup - Blood Tests
None required
Workup - Local Imaging
MRI with contrast of primary site
Workup - Biopsy
Excisional biopsy
Workup - Staging
Not required
Follow-up Summary
Medical disclaimer
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