CIC- Rearranged Sarcoma
Synonyms: CIC-DUX4 Sarcoma
Rapidly growing soft tissue mass
Quick Facts
Behaviour
Malignant
Category
Soft tissue
Grade
High
Synonyms
CIC-DUX4 Sarcoma
Category
Soft tissue
Behaviour
Malignant
Grade
High
Gender
Male
Tissue of Origin
Unknown
Epidemiology
- Rare high-grade round cell sarcoma
- Second most common Ewing-like sarcoma after Ewing sarcoma
- Young adults most commonly affected
Clinical Features
- Rapidly growing soft tissue mass
- Often large and deep-seated
- May present with pain
- Aggressive clinical behaviour
Location
- Deep soft tissues of trunk
- Extremities
- Retroperitoneum
Medical disclaimer
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