Benign Triton Tumour Ectomesenchymoma
Synonyms: Benign peripheral nerve sheath tumour with heterologous differentiation
Benign nerve sheath tumour variant
Quick Facts
Behaviour
Benign
Category
Soft tissue
Synonyms
Benign peripheral nerve sheath tumour with heterologous differentiation
Category
Soft tissue
Behaviour
Benign
Gender
M = F
Tissue of Origin
Neural
Epidemiology
- Benign nerve sheath tumour with skeletal muscle differentiation
- Rare
Clinical Features
Firm mass along nerve
Location
Any soft tissue site near nerves
Imaging
MRI: well-defined mass
Pathology
- Nerve sheath tumour with skeletal muscle differentiation
- Benign spindle cells and myogenic component
Genetics
Sporadic
Treatment
Surgical excision
Prognosis
Excellent - Benign
Key Points
Benign nerve sheath tumour variant
Workup - Blood Tests
No blood tests required
Workup - Local Imaging
MRI with contrast
Workup - Biopsy
Confirm diagnosis
Workup - Staging
No staging required
Medical disclaimer
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